1.02.d
Disorders of polyamine metabolism
- Ornithine decarboxylase superactivity (Bachmann-Bupp syndrome)
- Spermine synthase deficiency (Snyder-Robinson syndrome)
- Spermidine/spermine N(1)-acetyltransferase superactivity
- Methylthioadenosine phosphorylase deficiency (Diaphyseal medullary stenosis with malignant fibrous histiocytoma)
- Diaminopentanuria (Cystine-lysinuria)
Subnetworks
AOA
Aminoacid and organic acids related disorders
