1.3.b

Disorders of gluconeogenesis

  • Fructose-1,6-bisphosphatase deficiency
  • Pyruvate carboxylase deficiency
  • Cytosolic phosphoenolpyruvate carboxykinase deficiency
  • Mitochondrial phosphoenolpyruvate carboxykinase deficiency
  • Glycerol kinase deficiency

Subnetworks

cfao 1

C-FAO

Carbohydrate, fatty acid oxidation and ketone bodies disorders

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