3.1.c

Disorders of ectonucleotide and nucleic acid metabolism

  • 3′ repair exonuclease 1 deficiency (Aicardi-Goutières syndrome type 1; familial chilblain lupus; retinal vasculopathy with cerebral leukodystrophy)
  • Ribonuclease H2 subunit A deficiency (Aicardi-Goutières syndrome type 4)
  • Ribonuclease H2 subunit B deficiency (Aicardi-Goutières syndrome type 2)
  • Ribonuclease H2 subunit C deficiency (Aicardi-Goutières syndrome type 3)
  • Ribonuclease T2 deficiency (Cystic leukoencephalopathy without megalencephaly)
  • RNA-specific adenosine deaminase 1 deficiency (Aicardi-Goutières syndrome type 6, recessive; dyschromatosis symmetrica hereditaria, dominant)
  • RNA-specific adenosine deaminase 2 deficiency (Neurodevelopmental disorder with hypotonia, microcephaly, and seizures)
  • MDA5 superactivity (Aicardi-Goutières syndrome type 7; Singleton-Merten syndrome type 1)
  • STING superactivity (STING-associated vasculopathy with onset in infancy – SAVI)
  • 2′,5′-oligoadenylate synthetase 1 deficiency (Infantile-onset pulmonary alveolar proteinosis with hypogammaglobulinemia)
  • Activation-induced cytidine deaminase deficiency (Hyper-IgM syndrome type 2)
  • Uracil-DNA glycosylase deficiency (Hyper-IgM syndrome type 5)
  • ABCC6 deficiency (Generalized arterial calcification of infancy type 2, severe; pseudoxanthoma elasticum, milder)
  • Ectonucleotide pyrophosphatase/ phosphodiesterase 1 deficiency (Generalized arterial calcification of infancy type 1; autosomal recessive hypophosphatemic rickets type 2)
  • Ectonucleotide pyrophosphatase/ phosphodiesterase 1 dimerization deficiency (Cole disease)
  • Ectonucleoside triphosphate diphosphohydrolase 1 deficiency (Autosomal recessive spastic paraplegia type 64)
  • Ecto-5′-nucleotidase deficiency (Arterial calcification due to deficiency of CD73 – ACDC)
  • Ecto-5′-nucleotidase superactivity (Nucleotidase-associated pervasive developmental disorder)
  • Equilibrative nucleoside transporter 1 deficiency
  • Equilibrative nucleoside transporter 3 deficiency (H syndrome; familial Rosai-
  • Dorfman disease; Faisalabad histiocytosis)

Subnetworks

Immagini SNW 344 x 258 px 1

NOMS

Disorders of neuromodulators and other small molecules

Hey, want to upgrade to pro plan?

18748

Upgrade Now

& get 25% off

Offer valid only for 24 hrs.

18749
Scroll to Top